Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) pada anak

Abstract

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA)is a rare case of congenital coronary anomaly, potentially fatal and associeted with early death in infants and sudden death in adults. The incidence of this case is 1 in 300,000 live births. The pathophysiology of this syndrome causes the emergence of collateral circulation from the right coronary artery to the left coronary artery, which leads to myocardial ischemia and left ventricular dysfunction.The mitral valve regurgitation can also be found in the majority of patients, which is secondary to left ventricular dilatation and papillary muscle ischemia. Doppler Color-flow Echocardiography is one of the diagnostic investigations while cardiac catheterization and angiography are the gold standard for confirming the diagnosis of ALCAPA.Early diagnostic and surgical intervention can  confer a good prognosis in patients