BILATERAL MORGAGNI HERNIA IN INFANT, A RARE TYPE IN CONGENITAL DIAPHRAGMATIC HERNIA: A CASE SERIES
Abstract
Abstrak. Hernia Diafraghma Kongenital (HDK) merupakan kelainan kongenital yang jarang ditemukan pada bayi. Hernia Morgagni bilateral merupakan kasus yang sangat jarang ditemukan. Kami melaporkan kasus ini karena lokasi hernia Morgagni yang bilateral yang sangat jarang dijumpai (kanan dan kiri). Kami laporkan dua kasus dari HDK. Kasus pertama bayi perempuan usia 4 bulan dengan keluhan usus halus dan hati lobus kiri berada di dalam rongga dada yang berhubungan dengan defek anterior dari hernia diafraghma. Kasus kedua neonatus perempuan usia 22 hari datang dengan keluhan distress pernafasan, sesak nafas dan muntah. Pendekatan insisi subcotal dilakukan pada kedua pasien, dan defek dari hernia diafrahgma ditutup dengan menggunakan goretex pacth dengan hasil yang sangat baik. Pasca operasi, kedua pasien dengan kondisi sbaik, dan dipulangkan dari rumah sakit tanpa komplikasi. Berbagai macam teknik tindakan operasi telah dipaparkan, dan pendekatan dengan tindakan laparotomy telah menjadi salah satu standar teknik operasi. Tindakan ini dapat memungkinkan untuk mereduksi dan melihat isi dari hernia diafraghma tersebut, memudahkan untuk prosedur operasi dalam merepair bileteral hernia diafraghmatika. Dan sekaligus juga dapat mengkoreksi jika terdapat kelainan malrotasi dari usus halus. (JKS 2017; 2: 94-104)
Kata Kunci : Bilateral Morgagni Hernia, kondisi klinis non spesifik, pendekatan abdominal.
Abstract. Congenital diaphragmatic hernia (CDH) is a rare congenital anomaly in infant. Bilateral Morgagni Hernia is an absolute rarity. We describe this case because of the absolute rarity of bilateral localization in Morgagni hernia.We present 2 case series of CDH, First case a 4-month-old baby girl was an intrathoracic bowel and left lobe liver associated with anterior diaphragmatic defects in a symptomatic. Second case was a 22 days neonates girl, presented with respiratory distress, shortness of breath and vomiting. Subcostal incision were done for both patients, defect was repair with goretex pacth with a good result. Postoperatively, both of patient enjoyed an uneventful course and was discharged home without any further events. Numerous approaches have been described and, particularly the significance of laparatomy has been emphasized as an operative technique. This allows easy reduction and inspection of contents, allows access and repair of bilateral hernias, and corrects an associated malrotation if present. (JKS 2017; 2: 94-104)
Key Words : Bilateral Morgagni Hernia, Non spesific Presentations, Abdominal Approach.
Keywords
References
References
Oldham, et all, Congenital Diaphragmatic Hernia, in Oldham, Principles and and Practice of Pediatric Surgery Textbook, Chapter 58, Lippincott Williams & Wilkins, 2005, pp 354-66
Puri, Congenital Diaphragmatic Hernia and Eventration, in Puri, Pediatric Surgery Textbook, Chapter 13, Springer-Verlag Berlin Heidelberg, 2006, pp 115-24
Minneci, et all, Foramen of Morgagni Hernia: Changes in Diagnosis and Treatment, Ann Thorax Surg 2004 ;77:1956 –9
Robb, et all, Congenital Diaphragmatic Hernia Presenting as Splenic Rupture in an Adult, Ann Thorax Surg 2006 ;81:9 –10
Vicente, Congenital Diaphragmatic Hernia Bochdalek and Morgagni, Pediatric Surgery Handbook, Chapter 4, 2002, pp 19-21
Sbragia, et all, Congenital Diaphragmatic Hernia Without Herniation of the Liver: Does the Lung-to-Head Ratio Predict Survival? J Ultrasound Med 2000 ;19:845–848
Anynomious, Diaphragmatic Hernia, Centre for Arab Genomic Studies, 2005
Paek, et all, Congenital Diaphragmatic Hernia: prenatal Evaluation with MR Lung Volumetry-Preliminary Experience, Jurnal of Radiology 2001 ; 220:63–67
Jaillard, et all, Outcome at 2 Years of Infants With Congenital Diaphragmatic Hernia: A Population-Based Study, Ann Thorax Surg 2003 ;75:250–6
Tiruvoipati, et all, Predictors of outcome in patients with congenital diaphragmatic hernia requiring extracorporeal membrane oxygenation, Journal of Pediatric Surgery, 2007; 42, 1345–1350
Terzi, et all,A Rare Cause of Dyspnea in Adult: a Right Bochdalek’s Hernia-containing Colon, Asian Cardiovasc Thorax Ann 2008; 16:42–4
Goodfellow, et all, Congenital diaphragmatic hernia: the prognostic significance of the site of the stomach, The British Journal of Radiology, 1987, 60, 993-995
Rygl, et all, Acute Gastro-intestinal Obstruction as a Late Presentation of Congenital Diaphragmatic Hernia. A Report of Three Cases, Actachirbelg, 2006, 106, 430-432
Mallik, et all, Congenital Diaphragmatic Hernia: Experience in a Single Institution From 1978 Through 1994, Ann ThoracSurg1995;60:1331-1335
Deprest, et all, Current consequences of prenatal diagnosis of congenital diaphragmatic hernia, Journal of Pediatric Surgery, 2006; 41, 423–430
Eric, et all, Congenital Diaphragmatic Malformation, in Patterson, Pearson’s Thoracic and Esophageal Surgery Textbook, Third Edition Chapter 116, Churcill Livingstone Elsivier, 2009, pp 1401-1412
Armini, Bochdalek Hernia, download from www.webicina.com, 2008
Raymond, et all, Congenital Diaphragmatic Hernia with Malrotation of the Liver A Case Report, Dis Chest Journal, 1956; 29;583-584
Reynolds, Congenital Posterolateral Diaphragm Hernia’s and Other Less Common Hernia of the Diaphragm in Infant and Children, in Shields, General Thoracic Surgery Textbook, 7th Ed, Lippincot William and Wilkins, Chapter 53, 2009, pp 709-717
Krishna, et all, Laparoscopic repair of a congenital diaphragmatic hernia, Pediatr Surg Int 2002; 18: 491-493
Dalencourt, et all, Abdominal Compartment Syndrome After Late Repair of Bochdalek Hernia, Ann Thorax Surg 2006; 82:721–2
Hoyos, Foramen of Morgagni Hernia, in Shields, General Thoracic Surgery Textbook, 7th Ed, Lippincot William and Wilkins, Chapter 54, 2009, pp 719-724
Papanikolaou, et all, Bilateral Morgagni Hernia: Primary Repair without a Mesh, Case Rep Gastroenterol Journal, 2008;2:232–237
Lanteri, etall, Bilateral Morgagni-Larrey Hernia, Arch Surg. 2004;139:1299-1300.
Salem, Congenital hernia of Morgagni in infants and children. Journal of Pediatric Surgery, 2007, Sep;42(9):1539-43
Alper, et all, Bilateral Giant Morgagni Hernia Causing Cardiac Shifting, Trakya Univ Tip Fak Derg, 2009;26(1):74-77
Dingeldein, et all, Bilateral Intrathoracic Kidneys and Adrenal Glands associated With Posterior Congenital Diaphragmatic Hernias, Ann Thorax Surg 2008; 86:651-4
Young Ahn, et all, Prenatal Diagnosis of Congenital Diaphragmatic Hernia in a Fetus with 46,XY/46,X,-Y,+der(Y)t(Y;1)(q12;q12) Mosaicism : A Case Report ,J Korean Med Sci 2005; 20: 895-8
Takahashi,et all, Evaluating mortality and disease severity in congenital diaphragmatic hernia using the McGoon
and pulmonary artery, Journal of Pediatric Surgery, 2009; 44, 2101–2106
Uezono, The Japanese Approach to Congenital Diaphragmatic Hernia, Pediatr Surg 1999; 34:1813-7.
Fisher, et all, Redefining outcomes in right congenital diaphragmatic hernia, Journal of Pediatric Surgery, 2008; 43, 373–379
Nose, et all, Airway Anomalies in Patients With Congenital Diaphragmatic Hernia, Journal Pediatr Surg, 2000; 35:1562-1565
Thébaud, et all, Congenital diaphragmatic hernia: antenatal prognostic factors Does cardiac ventricular disproportion in utero predict outcome and pulmonary hypoplasia? Intensive Care Medicine Journal, 1997,pp1062-69
Silen, et all, Video-Assisted Thoracic Surgical Repair of a Foramen of Bochdalek Hernia, Ann Thorax Surg,1995;60:448-450
Grethel, et all, Prosthetic patches for congenital diaphragmatic hernia repair: Surgivis Gore-Tex, Journal of Pediatric Surgery, 2006; 41, 29– 33
Danzer, et all, Fetal tracheal occlusion for severe congenital diaphragmatic hernia in humans: a morphometric study of lung parenchyma and muscularization of pulmonary arterioles, Journal of Pediatric Surgery, 2008; 43, 1767–1775
Jean Deprest, et all, Prenatal Intervention for Congenital Diaphragm Hernia, in in Patterson, Pearson’s Thoracic and Esophageal Surgery Textbook, Third Edition Chapter 117, Churcill Livingstone Elsivier, 2009, pp 14013-1424
Jancelewicz, et all, Long-term surgical outcomes in congenital diaphragmatic hernia: observations from a single institution, Journal of Pediatric Surgery, 2010; 45, 155–160
DOI: 10.24815/jks.v17i2.8988
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